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Left ventricular noncompaction

Synonym(s) LVNC
Left ventricular hypertrabeculation
Spongy myocardium
Prevalence -
Inheritance Autosomal dominant
or X-linked recessive
or Mitochondrial inheritance
Age of onset All ages
  • I42.8
  • C1960469
MeSH -
MedDRA -


Disease definition

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.

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Detailed information

Clinical practice guidelines
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