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Budd-Chiari syndrome

Disease definition

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

ORPHA:131

  • Synonym(s): -
  • Prevalence: 1-9 / 100 000
  • Inheritance: Multigenic/multifactorial 
  • Age of onset: All ages
  • ICD-10: I82.0
  • OMIM: 600880
  • UMLS: C0856761
  • MeSH: D006502
  • GARD: 5968
  • MedDRA: 10006537

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