Cutis verticis gyrata

Orpha number	ORPHA671
Prevalence of rare diseases	Unknown
Inheritance	-
Age of onset	Variable
ICD 10 code	-
MIM number	-

Synonym(s)

Summary

Cutis verticis gyrata is a giant naevus of the scalp characterized by hypertrophy and thickening of the skin of the scalp forming burrows with deep and cerebriform cutaneous folds. Primitive cutis verticis gyrata involving the scalp only is genetically determined and usually associated with severe mental retardation. It must not be confused with plicae pachydermoperiostosis that affects the face and extremities (q.v.) and may involve the scalp.

Expert reviewer(s)

Dr Pascal REYGAGNE

Last update: May 2002

Suggest an update

(*) Required fields.

You are (*)

If you have selected the “Other” category, please specify which type of user you are: *

Email address: *

Topic of your comment: *

Epidemiology data

Clinical signs

Nomenclature and/or coding

Attention: Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Your message * (3000 characters remaining)

Check this box if you wish to receive a copy of your message

Please reproduce the text below

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.

Orphanet index

The portal for rare diseases and orphan drugs

Main menu :

Submenu :

Navigation tree :

Simple search

Other search option(s)

Cutis verticis gyrata

Summary

Expert reviewer(s)

Orphanet

Footer: