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Progressive non-fluent aphasia

ORPHA100070
Synonym(s) Agramatic variant of PPA
Agramatic variant of primary progressive aphasia
Non-fluent variant PPA
Prevalence 1-9 / 100 000
Inheritance Multigenic/multifactorial
or Not applicable
Age of onset Adult
ICD-10
  • G31.0
OMIM
UMLS
  • C0751706
MeSH
  • D057178
MedDRA
  • 10029542

Summary

Progressive non-fluent aphasia (PNFA) is a form of frontotemporal dementia (FTD; see this term), characterized by agrammatism, laborious speech, alexia, and agraphia, frequently accompanied by apraxia of speech (AOS). Language comprehension is relatively preserved.


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Detailed information

Article for general public
  • FR (2007,pdf)
Clinical genetics review
  • EN (2007)
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