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Autoimmune pancreatitis

Orpha number ORPHA103919
Synonym(s) AIP
Prevalence -
Inheritance -
Age of onset -
ICD-10
  • K86.1
ICD-O -
OMIM -
UMLS
  • C2609129
MeSH -
MedDRA
  • 10069002
SNOMED CT
  • 448542008

Summary

Autoimmune pancreatitis (AIP) is a rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type 1 AIP (see this term) which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2 AIP (see this term) which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.


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Detailed information

Review article
  • EN (2014)
Diagnostic criteria
  • EN (2014,pdf)
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