Orphanet: Chordoma

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.


Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Captcha image


Disease definition

Chordomas are rare malignant tumors arising from embryonic remnants of the notochord in axial skeleton.


  • Synonym(s):
    • Notochordal sarcoma
  • Prevalence: -
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: Adult
  • ICD-10: C76.7
  • OMIM: 215400
  • UMLS: C0008487
  • MeSH: D002817
  • GARD: 1303
  • MedDRA: 10008747

Detailed information


Additional information

Further information on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.