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Arrhythmogenic right ventricular dysplasia

Synonym(s) ARVC
Arrhythmogenic right ventricular cardiomyopathy
Prevalence 1-5 / 10 000
Inheritance Autosomal dominant
or Autosomal recessive
Age of onset Adult
  • I42.8
  • C0349788
  • D019571
  • 10058093


Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias. and progressive right ventricular or biventricular failure. ARCVD is a major cause of sudden death in the young and among athletes.

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