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Rare lichen planus

Orpha number ORPHA254367
Synonym(s) Rare LP
Prevalence Unknown
Inheritance -
Age of onset Variable
ICD-10
  • L43.0
  • L43.1
  • L43.2
  • L43.3
  • L43.8
  • L43.9
  • L66.1
OMIM
UMLS -
MeSH -
MedDRA -
SNOMED CT -

Summary

Lichen planus (LP) is a common inflammatory dermatosis characterized by the development of pruritic violaceous papules or plaques on mucocutaneous surfaces. Eruptions can involve the face, neck, limbs, back, genitalia, tongue, buccal mucosa, nails, and scalp. LP comprises rare variants affecting the skin and the mucosa. Rare cutaneous LP includes linear LP (referring to blaschkoid and zosteriform distributions of lichenoid lesions), actinic LP, annular LP, atrophic LP, annular atrophic LP, lichen planopilaris (comprising Graham Little-Piccardi-Lassueur syndrome and frontal fibrosing alopecia), lichen planus pigmentosus, and lichen planus pemphigoides (see these terms). Rare mucosal LP includes vulvovaginal gingival syndrome and LP sialadenitis (see these terms).

Expert reviewer(s)

  • Dr Stephanie ARNOLD
  • Dr Susan COOPER

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