x

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.

Attention

Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Captcha image

Sézary syndrome

Disease definition

Sézary syndrome (SS) is an aggressive form of cutaneous T-cell lymphoma characterized by a triad of erythroderma, lymphadenopathy and circulating atypical lymphocytes (Sézary cells).

ORPHA:3162

  • Synonym(s):
    • Sézary lymphoma
  • Prevalence: Unknown
  • Inheritance: Not applicable or Multigenic/multifactorial 
  • Age of onset: Adult
  • ICD-10: C84.1
  • OMIM: -
  • UMLS: C0036920
  • MeSH: D012751
  • GARD: 7629
  • MedDRA: 10040493

Detailed information

Professionals

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.