x

Search for a rare disease

* (*) mandatory field
Suggest an update

(*) Required fields.

Attention: Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.


Captcha image

Granulomatosis with polyangiitis

Disease definition

Wegener granulomatosis is a small-vessel necrotizing vasculitis characterised by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis.

ORPHA:900

  • Synonym(s):
    • GPA
    • Wegener granulomatosis
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: M31.3
  • OMIM: 608710
  • UMLS: C0043092
  • MeSH: D014890
  • GARD: 7880
  • MedDRA: 10047888
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.