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Indolent systemic mastocytosis

Disease definition

Indolent systemic mastocytosis (ISM) is a benign form of systemic mastocytosis (SM; see this term) characterized by an abnormal proliferation of mast cells either only in bone marrow or in numerous tissues.

ORPHA:98848

  • Synonym(s): -
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: D47.0
  • OMIM: -
  • UMLS: C0272203
  • MeSH: -
  • GARD: -
  • MedDRA: 10056452

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