Partenariat : Académiques =
, Industriels =
, Investisseurs financiers = 
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- EUCILIA: generation and characterization of in vitro models to study the role of BBS, OFD1 and NPHP in the formation and function of the primary cilium (WP2)
- Universitätsklinikum Freiburg
- The Walz lab - Hereditary Kidney Diseases - Molecular Biology
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- EUCILIA: the role of BBS, OFD1, and NPHP proteins in Wnt signalling, tubulogenesis and cyst formation (WP4)
- Universitätsklinikum Freiburg
- The Walz lab - Hereditary Kidney Diseases - Molecular Biology
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- SYSCILIA - Component 3 - "Assessing and manipulating the variables of ciliary systems" (WP5)
- Universitätsklinikum Freiburg
- The Walz lab - Hereditary Kidney Diseases - Molecular Biology
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- EUCILIA: generation and characterization of in vitro models to study the role of BBS, OFD1 and NPHP in the formation and function of the primary cilium (WP2)
- Universitätsklinikum Freiburg
- Arbeitsgruppe Professor Dr. med. Heymut Omran
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- EUCILIA: the role of BBS, OFD1, and NPHP proteins in Wnt signalling, tubulogenesis and cyst formation (WP4)
- Universitätsklinikum Freiburg
- Arbeitsgruppe Professor Dr. med. Heymut Omran
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- SKELNET - Skeletal Dysplasia Network (coordination)
- Universitätsklinikum Freiburg
- Geschäftsstelle SKELNET e.V.
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- FREIBURG
- FACE - molecular pathology of craniofacial ciliopathies (subproject 1)
- Universitätsklinikum Freiburg
- FZSE - Freiburg Zentrum für Seltene Erkrankungen
- Plus de détails
-
- ALLEMAGNE
- Baden-Württemberg
- TÜBINGEN
- SYSCILIA - Component 1 -"Defining the elements and variables of ciliary systems" (WP1 and WP2)
- Universität Tübingen
- Forschungsinstitut für Augenheilkunde
- Plus de détails
-
- ALLEMAGNE
- Nordrhein-Westfalen
- ESSEN
- SKELNET : Chondrocyte specific genes as part of the signaling regulation of chondrocyte differentiation
- Universität Duisburg-Essen
- Abteilung Entwicklungsbiologie
- Plus de détails
-
- Diagnosis and management of ectodermal dysplasia in neonates and infants
- Medizinische Universität Innsbruck
- Stoffwechsellabor der Universitätsklinik für Kinder- und Jugendheilkunde
- Plus de détails
-
- BELGIQUE
- ARRONDISSEMENT BRUSSELS-CAPITAL
- BRUXELLES
- EUROGROW: Pathophysiology of various osteochondrodysplasias by studying the cartilage growth plate in transgenic mice models
- Université Catholique de Louvain - UCL
- European network for the study of orphan nephropathies
- Plus de détails
-
- CANADA
- Colombie-Britannique
- VANCOUVER
- FORGE - Finding of Rare Disease Genes in Canada
- University of British Columbia
- Faculty of Medicine
- Plus de détails
-
- CANADA
- Ontario
- OTTAWA, ONTARIO
- FORGE - Finding of Rare Disease Genes in Canada
- University of Ottawa
- Faculty of Medicine -
- Plus de détails
-
- FORGE - Finding of Rare Disease Genes in Canada
- Centre hospitalier universitaire Sainte-Justine
- Pédiatrie
- Plus de détails
-
- ESPAGNE
- Comunidad Valenciana
- VALENCIA
- Molecular foundations of the human ectodermic dysplasia syndrome
- Instituto de Biomedicina de Valencia (CSIC)
- Unidad de Modelos Animales de Patologías Cutáneas
- Plus de détails
-
- Genetic and molecular bases of pathology of Ellis-van Creveld syndrome and Weyers acrodental dysostosis
- Instituto de Investigaciones Biomédicas "Alberto Sols" (CSIC-UAM)
- Genética de las Enfermedades Hereditarias: Desarrollo y Enfermedad
- Plus de détails
-
- Molecular analysis of the Ellis-van Creveld Syndrome in the EVC3 epiphyseal growth plate
- Instituto de Investigaciones Biomédicas "Alberto Sols" (CSIC-UAM)
- Genética de las Enfermedades Hereditarias: Desarrollo y Enfermedad
- Plus de détails
-
- FRANCE
- ILE-DE-FRANCE
- PARIS
- Dysplasies ectodermiques et incontinentia pigmenti: démembrement clinique et génétique; étude des mécanismes physiopathologiques
- CHU Paris - Hôpital Necker - Enfants Malades
- MAGEC - Service de dermatologie
- Plus de détails
-
- ITALIE
- ABRUZZO
- SANTA MARIA IMBARO
- EUCILIA: study of the ciliary protein interaction network to establish a hierarchy of temporal and spatial interactions of BBS, OFD1, and NPHP proteins (WP3)
- Consorzio Mario Negri Sud
- Dipartimento di Biologia Cellulare e Oncologia
- Plus de détails
-
- EUCILIA: thorough analysis of animal models with mutant BBS, OFD1, or NPHP protein (WP1)
- TIGEM - Telethon Institute of Genetics and Medicine
- Laboratorio di Ricerca
- Plus de détails
-
- Atrioventricular Canal Defect as a Sign of Laterality Defect in Ellis-van Creveld and Polydactyly Syndromes With Ciliary and Hedgehog Signaling Dysfunction
- IRCCS Ospedale Pediatrico Bambino Gesù
- U.O. di Genetica Medica
- Plus de détails
-
- Atrioventricular Canal Defect as a Sign of Laterality Defect in Ellis-van Creveld and Polydactyly Syndromes With Ciliary and Hedgehog Signaling Dysfunction
- IRCCS Ospedale Pediatrico Bambino Gesù
- Servizio Clinico di Consulenza Genetica
- Plus de détails
-
- GENESKIN: European network on rare genetic skin diseases (coordination)
- Istituto Dermopatico dell'Immacolata - IRCCS
- Laboratorio di Biologia Molecolare e Cellulare
- Plus de détails
-
- Atrioventricular Canal Defect as a Sign of Laterality Defect in Ellis-van Creveld and Polydactyly Syndromes With Ciliary and Hedgehog Signaling Dysfunction
- Sapienza Università di Roma - Policlinico Umberto I
- Dipartimento di Pediatria
- Plus de détails
-
- ROYAUME-UNI
- Greater London
- LONDON
- Natural history and management in Skeletal Dysplasias
- Great Ormond Street Hospital for Children NHS Foundation Trust
- Clinical Genetics
- Plus de détails
-
- ROYAUME-UNI
- Greater London
- LONDON
- EUCILIA: study of the downstream events caused by the absence of BBS, OFD1, or NPHP (WP5)
- UCL Institute of Child Health
- Molecular Medicine Unit
- Plus de détails
-
- ROYAUME-UNI
- Greater London
- LONDON
- EUCILIA: identification of druggable targets for the amelioration and prevention of rare diseases due to ciliary dysfunction: nephronophthisis, Oral-facial-digital type 1 and Bardet-Biedl syndromes, in fish and mouse models (WP6)
- UCL Institute of Child Health
- Molecular Medicine Unit
- Plus de détails
-
- ROYAUME-UNI
- Greater Manchester
- MANCHESTER
- ESDN: European Skeletal Dysplasia Network (coordination)
- Faculty of Life Sciences - University of Manchester
- Wellcome Trust Centre for Cell Matrix Research
- Plus de détails