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Kaposi sarcoma

Disease definition

A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C46.0  C46.1  C46.2  C46.3  C46.7  C46.8  C46.9
  • OMIM: 148000
  • UMLS: C0036220
  • MeSH: D012514
  • GARD: 6814
  • MedDRA: 10023284

Detailed information

Article for general public


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