Orphanet: Hereditary papillary renal cell carcinoma

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Hereditary papillary renal cell carcinoma

Disease definition

Hereditary papillary renal cell carcinoma (HPRCC) is a familial renal cancer syndrome characterised by a predisposition for developing bilateral and multifocal type 1 papillary renal carcinomas.


Classification level: Disorder
  • Synonym(s):
    • HPRCC
  • Prevalence: -
  • Inheritance: Autosomal dominant 
  • Age of onset: Adult
  • ICD-10: C64
  • OMIM: 605074
  • UMLS: C0879257  C2931899
  • MeSH: C538614
  • GARD: -
  • MedDRA: -

Detailed information

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