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Nodular regenerative hyperplasia of the liver

Disease definition

A form of portosinusoidal vascular disease characterized histologically by the absence of cirrhosis and diffuse benign transformation of the hepatic parenchyma into multiple small nodules (typically 1-3 mm).

ORPHA:48372

Classification level: Subtype of disorder
  • Synonym(s):
    • Non-cirrhotic nodulation
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: K76.8
  • ICD-11: DB98.2
  • OMIM: -
  • UMLS: -
  • MeSH: -
  • GARD: 10929
  • MedDRA: -

  A summary on this disease is available in Español (2015) Italiano (2015) Français (2021) Nederlands (2021) Português (2021) Deutsch (2003)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

Newborn screening

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