Orphanet: Idiopathic bronchiectasis

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Idiopathic bronchiectasis

Disease definition

Idiopathic bronchiectasis (IB) is a progressive lung disease characterized by chronic dilation of the bronchi and destruction of the bronchial walls in the absence of any underlying cause (such as post infectious disease, aspiration, immunodeficiency, congenital abnormalities and ciliary anomalies).


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: -
  • Inheritance: -
  • Age of onset: All ages
  • ICD-10: J47
  • OMIM: 211400  613021  613071
  • UMLS: C0339985
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


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