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Congenital heart block

Disease definition

Congenital heart block (CHB) is a rare disorder of atrioventricular conduction, characterized by absence of conduction of atrial impulses to the ventricles with slower ventricular rhythm (atrioventricular dissociation). CHB can occur in association with immunological evidence of maternal connective disease (autoimmune CHD), fetal structural CHD or can be idiopathic.


Classification level: Disorder
  • Synonym(s):
    • Congenital atrioventricular block
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Infancy, Neonatal
  • ICD-10: Q24.6
  • ICD-11: LA8Y
  • OMIM: 234700
  • UMLS: C0149530  C3884338
  • MeSH: C535758
  • GARD: 6164
  • MedDRA: 10019263

Detailed information


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