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Respiratory bronchiolitis-interstitial lung disease syndrome

Disease definition

Respiratory bronchiolitis - interstitial lung disease is a mild inflammatory pulmonary disorder developed by cigarette smokers and characterized by shortness of breath and cough, pulmonary function abnormalities of mixed restrictive and obstructive lung disease and high resolution CT scanning showing centrilobular micronodules, ground glass opacities and peribronchiolar thickening.


Classification level: Disorder
  • Synonym(s):
    • RB-ILD
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: J68.4
  • OMIM: -
  • UMLS: C1276236  C1735355
  • MeSH: -
  • GARD: -
  • MedDRA: 10066393

Detailed information


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