Orphanet: Mastocytose cutanée maculopapulaire

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Maculopapular cutaneous mastocytosis

Disease definition

Maculopapular cutaneous mastocytosis (MCM) is a form of cutaneous mastocytosis (CM; see this term) characterized by the presence of multiple hyperpigmented macules, papules or nodules associated with abnormal accumulation of mast cells in the skin.


Classification level: Disorder
  • Synonym(s):
    • Urticaria pigmentosa
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: Q82.2
  • OMIM: 154800
  • UMLS: C0042111
  • MeSH: D014582
  • GARD: -
  • MedDRA: 10046752

Detailed information

Article for general public


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