Orphanet: Renal dysplasia, unilateral

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Renal dysplasia, unilateral

Disease definition

Unilateral renal dysplasia is a form of renal dysplasia (RD; see this term), a renal tract malformation in which the development of one kidney is abnormal and incomplete. Unilateral RD can be segmental, and of variable severity, with renal aplasia corresponding to extreme RD.


Classification level: Subtype of disorder
  • Synonym(s):
    • Kidney dysplasia, unilateral
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable or Autosomal dominant 
  • Age of onset: All ages
  • ICD-10: Q61.4
  • OMIM: -
  • UMLS: C0431697
  • MeSH: -
  • GARD: -
  • MedDRA: -
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