Orphanet: Unilateral multicystic dysplastic kidney

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Unilateral multicystic dysplastic kidney

Disease definition

A rare form of multicystic dysplastic kidney (MCDK), a congenital anomaly of the kidney and urinary tract (CAKUT), in which one kidney is large, distended by multiple cysts, and non-functional.


Classification level: Subtype of disorder
  • Synonym(s):
    • Unilateral MCDK
    • Unilateral multicystic renal dysplasia
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant 
  • Age of onset: All ages
  • ICD-10: Q61.4
  • OMIM: -
  • UMLS: C1567426
  • MeSH: D021782
  • GARD: -
  • MedDRA: -

Detailed information


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