Orphanet: Bilateral multicystic dysplastic kidney

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Bilateral multicystic dysplastic kidney

Disease definition

A rare lethal form of multicystic dysplastic kidney (MCDK), a congenital anomaly of the kidney and urinary tract (CAKUT), in which both kidneys are large, distended by non-communicating multiple cysts and non-functional.


Classification level: Subtype of disorder
  • Synonym(s):
    • Bilateral MCDK
    • Bilateral multicystic renal dysplasia
  • Prevalence: Unknown
  • Inheritance: -
  • Age of onset: Antenatal, Neonatal
  • ICD-10: Q61.4
  • OMIM: -
  • UMLS: C1567427  C1840451
  • MeSH: C537373  D021782
  • GARD: 9517
  • MedDRA: -

Detailed information


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