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Systemic mastocytosis with an associated clonal hematologic non-mast cell lineage disease

Disease definition

Systemic mastocytosis with an associated clonal hematological non-mast cell lineage disease is a form of systemic mastocytosis (SM) associated with malignancy (other than mast cell leukemia).


  • Synonym(s):
    • SM-AHN
    • SM-AHNMD
    • Systemic mastocytosis with associated hematologic neoplasm
  • Prevalence: 1-9 / 1 000 000
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C96.2
  • OMIM: -
  • UMLS: C1301365
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

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Additional information

Further information on this disease

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