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Primary central nervous system vasculitis


  • Synonym(s):
    • Isolated angiitis of the central nervous system
    • PACNS
    • PCNSV
    • Primary angiitis of the central nervous system
    • Primary vasculitis of the central nervous system
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: I67.7
  • OMIM: -
  • UMLS: C0751881  C2930862
  • MeSH: C535276  D020293
  • GARD: 8703
  • MedDRA: -

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