Orphanet: Acral peeling skin syndrome

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.


Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Captcha image

Acral peeling skin syndrome

Disease definition

A rare peeling skin syndrome characterized by superficial peeling of the skin predominantly affecting the dorsa of the hands and feet.


Classification level: Disorder
  • Synonym(s):
    • Acral PSS
    • Acral deciduous skin
    • Localized PSS
    • Localized deciduous skin
  • Prevalence: <1 / 1 000 000
  • Inheritance: Autosomal recessive 
  • Age of onset: Infancy, Neonatal
  • ICD-10: Q80.8
  • OMIM: 609796
  • UMLS: C1853354
  • MeSH: -
  • GARD: 12863
  • MedDRA: -

Detailed information


The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.