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Autoimmune pancreatitis type 1
Disease definition
Type 1 autoimmune pancreatitis is a form of autoimmune pancreatitis seen in elderly males (>60 years) and presenting with abdominal pain, steatorrhea, obstructive jaundice and other organ (bile duct, kidneys and retroperitoneum) involvement. It is thought to be due to an immunoglobulin G4 (IgG4)-associated systemic disease.
ORPHA:280302
Classification level: Subtype of disorder- Synonym(s):
- AIP type 1
- IgG4-related pancreatitis
- Lymphoplasmacytic sclerosing pancreatitis
- Prevalence: Unknown
- Inheritance: Not applicable
- Age of onset: Adult
- ICD-10: K86.1
- OMIM: -
- UMLS: -
- MeSH: -
- GARD: -
- MedDRA: -
Detailed information
Article for general public
Professionals
- Summary information
- Japanese (2019, pdf)
- Review article
- English (2011)
- Diagnostic criteria
- English (2014, pdf)
Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
Specialised Social Services
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.