Search for a rare disease
Other search option(s)
Inherited isolated arrhythmogenic cardiomyopathy, dominant-left variant
ORPHA:293888
Classification level: Subtype of disorder- Synonym(s):
- ALVC
- Arrhythmogenic cardiomyopathy dominant-left variant
- Arrhythmogenic cardiomyopathy with left ventricular involvement
- Familial isolated arrhythmogenic ventricular dysplasia, left-dominant form
- Prevalence: -
- Inheritance: -
- Age of onset: -
- ICD-10: I42.8
- ICD-11: BC43.6
- OMIM: 107970 610193
- UMLS: C5679933
- MeSH: -
- GARD: -
- MedDRA: -
Summary
This disease is described under Inherited isolated arrhythmogenic cardiomyopathy
Detailed information
Guidelines
- Emergency guidelines
- Français (2019, pdf) - Orphanet Urgences
- Clinical practice guidelines
- English (2019) - Heart Rhythm
- Français (2022) - PNDS
Disease review articles
- Review article
- English (2016) - Orphanet J Rare Dis
- Clinical genetics review
- English (2017) - GeneReviews


Additional information
Further information on this disease
Patient-centred resources for this disease
Research activities on this disease
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.