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Clear cell renal carcinoma

Disease definition

A rare renal tumor arising from proximal tubular epithelial cells of the renal cortex, characterized histologically by malignant epithelial cells with typical clear cytoplasm in conventional staining methods due to a high glycogen and lipid content, featuring a nested growth pattern. Clinically it may present with hematuria, flank pain, anemia or, less commonly, a palpable abdominal mass.


Classification level: Disorder
  • Synonym(s):
    • CCRCC
    • Clear cell renal cell adenocarcinoma
    • Clear cell renal cell carcinoma
  • Prevalence: -
  • Inheritance: -
  • Age of onset: Adult, Elderly
  • ICD-10: C64
  • OMIM: -
  • UMLS: C0279702
  • MeSH: -
  • GARD: 9574
  • MedDRA: -

Detailed information


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