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Hereditary nonpolyposis colon cancer

Disease definition

A cancer-predisposing condition characterized by the development of colorectal cancer not associated with colorectal polyposis, endometrial cancer, and various other cancers (such as malignant epithelial tumor of ovary, gastric, biliary tract, small bowel, and urinary tract cancer) that are frequently diagnosed at an early age.


Classification level: Group of disorders
  • Synonym(s):
    • Familial nonpolyposis colon cancer
    • Familial nonpolyposis colorectal cancer
    • HNPCC
    • Hereditary nonpolyposis colorectal cancer
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: -
  • OMIM: -
  • UMLS: C0009405  C1112155  C1333990
  • MeSH: -
  • GARD: 8533
  • MedDRA: -

Detailed information

Article for general public


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