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Insulin-resistance syndrome type B

Disease definition

A rare genetic disease that belongs to the group of extreme insulin-resistance syndromes and is due to autoantibodies directed against insulin receptor.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult, Childhood, Adolescent, Elderly
  • ICD-10: E13
  • OMIM: -
  • UMLS: C0342337
  • MeSH: -
  • GARD: 3009
  • MedDRA: -

Detailed information


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