Orphanet: Eosinophilic granulomatosis with polyangiitis

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Eosinophilic granulomatosis with polyangiitis

Disease definition

Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.


Classification level: Disorder
  • Synonym(s):
    • Churg-Strauss syndrome
    • EGPA
    • Granulomatous allergic angiitis
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Adolescent, Adult, Elderly
  • ICD-10: M30.1
  • OMIM: -
  • UMLS: C0008728
  • MeSH: C531653  D015267
  • GARD: 6111
  • MedDRA: 10048594

Detailed information


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