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Kawasaki disease

Disease definition

A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated.


Classification level: Disorder
  • Synonym(s):
    • Mucocutaneous lymph node syndrome
  • Prevalence: Unknown
  • Inheritance: Multigenic/multifactorial 
  • Age of onset: Adult, Infancy, Childhood, Adolescent
  • ICD-10: M30.3
  • OMIM: 611775
  • UMLS: C0026691
  • MeSH: -
  • GARD: 6816
  • MedDRA: 10023320
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