Orphanet: Pemphigus vulgaire

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Pemphigus vulgaris

Disease definition

A rare autoimmune bullous skin diseases characterized by painful, flaccid blisters and erosions of the oral mucosa, predominantly involving the buccal area, and with or without extension to the epidermis. Mucosa of the larynx, oesophagus, conjunctiva, nose, genitalia and anus, are less frequently affected.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: L10.0
  • OMIM: 169610
  • UMLS: C0030809
  • MeSH: -
  • GARD: 7355
  • MedDRA: 10052802

Detailed information

Article for general public


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