Orphanet: Pemphigus vulgaris

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Pemphigus vulgaris

Disease definition

Pemphigus is a group of chronic autoimmune skin diseases characterized by blister formations on the outer layer of the skin and the mucous membranes. Three clinical forms have been characterised, of which pemphigus vulgaris is the most frequent (75%).


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: 1-5 / 10 000
  • Inheritance: Not applicable 
  • Age of onset: Adult, Elderly
  • ICD-10: L10.0
  • OMIM: 169610
  • UMLS: C0030809
  • MeSH: -
  • GARD: 7355
  • MedDRA: 10052802

Detailed information

Article for general public


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