Orphanet: Leiomyosarcoma of small intestine

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Leiomyosarcoma of small intestine

Disease definition

Small bowel leiomyosarcoma is a rare type of small bowel malignancy, originating in the smooth muscle cells within the muscularis propria or the muscularis mucosa, most often found in the jejunum, and presenting with gastrointestinal bleeding and anemia and sometimes with other non-specific symptoms such as vomiting, nausea, abdominal pain and weakness and spreading to regional lymph nodes in 14% of cases.


Classification level: Disorder
  • Synonym(s): -
  • Prevalence: -
  • Inheritance: -
  • Age of onset: -
  • ICD-10: C17.0  C17.1  C17.2  C17.3  C17.8
  • OMIM: -
  • UMLS: C0920305
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information


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