Orphanet: Juvenile Huntington disease

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Juvenile Huntington disease

Disease definition

Juvenile Huntington disease (JHD) is a form of Huntington disease (HD; see this term), characterized by onset of signs and symptoms before 20 years of age.


Classification level: Disorder
  • Synonym(s):
    • JHD
    • Juvenile Huntington chorea
  • Prevalence: 1-9 / 1 000 000
  • Inheritance: Autosomal dominant 
  • Age of onset: Adolescent, Childhood
  • ICD-10: G10
  • OMIM: 143100
  • UMLS: C0751208
  • MeSH: -
  • GARD: 10510
  • MedDRA: -

Detailed information

Article for general public

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