Orphanet: Congenital factor V deficiency

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Congenital factor V deficiency

Disease definition

Congenital factor V deficiency is an inherited bleeding disorder due to reduced plasma levels of factor V (FV) and characterized by mild to severe bleeding symptoms.


Classification level: Disorder
  • Synonym(s):
    • Owren disease
    • Parahemophilia
    • Proaccelerin deficiency
  • Prevalence: 1-9 / 1 000 000
  • Inheritance: Autosomal recessive 
  • Age of onset: All ages
  • ICD-10: D68.2
  • OMIM: 227400
  • UMLS: C0015499
  • MeSH: -
  • GARD: 2237
  • MedDRA: 10048930

Detailed information

Article for general public


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