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Intraductal papillary mucinous carcinoma of pancreas

Disease definition

Intraductal papillary mucinous carcinoma of pancreas is a rare epithelial tumor of pancreas characterized by malignant, mucin-producing cystic mass, originating from the pancreatic ductal system, associated with local invasion and metastatic spread, composed of mucin-producing, columnar epithelial cells covering the dilated pancreatic ducts with a papillary structure. The presenting symptoms are non-specific and include abdominal pain, pancreatitis, steatorrhea, jaundice and diabetes. Many patients are asymptomatic at the time of diagnosis.


Classification level: Disorder
  • Synonym(s):
    • IPMN
    • Pancreatic intraductal papillary mucinous carcinoma
  • Prevalence: -
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C25.3
  • ICD-11: 2C10.0
  • OMIM: -
  • UMLS: C1335304
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

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Disease review articles

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