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Foix-Alajouanine syndrome

Disease definition

Foix-Alajouanine syndrome, also called subacute ascending necrotising myelitis, results from chronic congestion of the extrinsic pial veins of the spinal cord and of the intrinsic subpial network. It is characterised by progressive ascending deficit over a period of several months or years.

ORPHA:79093

Classification level: Disorder
  • Synonym(s):
    • Angiodysgenetic necrotizing myelopathy
    • Familial osteosclerosis with abnormalities of the nervous system and meninges
    • Subacute angiohypertrophic myelomalacia
    • Subacute ascending necrotizing myelitis
    • Subacute necrotizing myelitis
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: G37.4
  • ICD-11: 8A45.21
  • OMIM: -
  • UMLS: C0348023  C0472347
  • MeSH: -
  • GARD: -
  • MedDRA: -
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