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Congenitally uncorrected transposition of the great arteries

Disease definition

Congenitally uncorrected transposition of the great arteries (congenitally uncorrected TGA), also referred to as complete transposition, is a congenital cardiac malformation characterized by atrioventricular concordance and ventriculoarterial (VA) discordance.


Classification level: Disorder
  • Synonym(s):
    • Congenitally uncorrected transposition of the great vessels
    • D-transposition of the great arteries
    • Dextro-transposition of the great arteries
    • Isolated ventriculoarterial discordance
    • Ventriculoarterial discordance with atrioventricular concordance
  • Prevalence: Unknown
  • Inheritance: Multigenic/multifactorial or Not applicable 
  • Age of onset: Infancy, Neonatal
  • ICD-10: Q20.3
  • ICD-11: LA85.1
  • OMIM: 608808  613854
  • UMLS: C3531771
  • MeSH: -
  • GARD: -
  • MedDRA: -

Detailed information

General public


Disease review articles

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