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Generalized pustular psoriasis

Disease definition

Generalized pustular psoriasis is a severe inflammatory skin disease that can be life-threatening and that is characterized by recurrent episodes of high fever, fatigue, episodic erythematous cutaneous eruptions with sterile cutaneous pustules formation on various parts of the body, and neutrophil leukocytosis.

ORPHA:247353

Classification level: Disorder
  • Synonym(s):
    • GPP
  • Prevalence: 1-9 / 1 000 000
  • Inheritance: Autosomal recessive or Not applicable 
  • Age of onset: Adult
  • ICD-10: L40.1
  • ICD-11: EA90.40
  • OMIM: 614204  616106
  • UMLS: C0343055
  • MeSH: -
  • GARD: 12819
  • MedDRA: -

  A summary on this disease is available in Deutsch (2012) Español (2012) Français (2012) Italiano (2012) Nederlands (2012) Greek (2012, pdf)

Detailed information

Disease review articles

ERN produced/endorsed by ERN(s)   FSMR produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.