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Systemic-onset juvenile idiopathic arthritis

Disease definition

Systemic-onset juvenile idiopathic arthritis is marked by the severity of the extra-articular manifestations (fever, cutaneous eruptions) and by an equal sex ratio.


  • Synonym(s):
    • Still disease
    • Systemic polyarthritis
    • Systemic-onset JIA
  • Prevalence: 1-9 / 100 000
  • Inheritance: Unknown or Multigenic/multifactorial 
  • Age of onset: Childhood
  • ICD-10: M08.2
  • OMIM: 604302
  • UMLS: C0087031  C1384600
  • MeSH: -
  • GARD: 10966
  • MedDRA: -
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