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Juvenile dermatomyositis

Disease definition

An early-onset form of dermatomyositis (DM), a systemic, autoimmune inflammatory muscle disorder with vasculopathy, characterized by proximal and symmetrical muscle weakness, evocative skin lesions, and systemic manifestations. Vasculopathy occurs in the skin, muscle (mainly in the perifascicular area), and sometimes in the intestinal tissue.


Classification level: Disorder
  • Synonym(s):
    • Juvenile DM
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: Infancy, Childhood, Adolescent
  • ICD-10: M33.0
  • ICD-11: 4A41.01
  • OMIM: -
  • UMLS: C0263666  C2931785
  • MeSH: C538250
  • GARD: 6805
  • MedDRA: 10008521
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.