Orphanet: Idiopathic ventricular fibrillation, non Brugada type
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Idiopathic ventricular fibrillation, non Brugada type

Disease definition

A rare, genetic, cardiac rhythm disease characterized by ventricular fibrillation in the absence of any structural or functional heart disease, or known repolarization abnormalities. The presence of J waves is associated with a higher risk of nocturnal ventricular fibrillation events and a higher risk of recurrence.

ORPHA:228140

Classification level: Disorder
  • Synonym(s):
    • Familial paroxysmal ventricular fibrillation, non Brugada type
  • Prevalence: Unknown
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: All ages
  • ICD-10: I49.0
  • OMIM: 603829  612956
  • UMLS: -
  • MeSH: -
  • GARD: 4227
  • MedDRA: -

  A summary on this disease is available in Deutsch (2019) Español (2019) Français (2019) Italiano (2019) Nederlands (2019)

Detailed information

Guidelines

Genetic Testing

ERN : produced/endorsed by ERN(s)
FSMR : produced/endorsed by FSMR(s)

Additional information

Further information on this disease

Patient-centred resources for this disease

Research activities on this disease

Specialised Social Services

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