Orphanet: Sézary syndrome

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Sézary syndrome

Disease definition

Sézary syndrome (SS) is an aggressive form of cutaneous T-cell lymphoma characterized by a triad of erythroderma, lymphadenopathy and circulating atypical lymphocytes (Sézary cells).


Classification level: Disorder
  • Synonym(s):
    • Sézary lymphoma
  • Prevalence: Unknown
  • Inheritance: Not applicable or Multigenic/multifactorial 
  • Age of onset: Adult
  • ICD-10: C84.1
  • OMIM: -
  • UMLS: C0036920
  • MeSH: D012751
  • GARD: 7629
  • MedDRA: 10040493

Detailed information


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