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Bullous lichen planus
Disease definition
Bullous lichen planus is a variant of rare lichen planus (see this term) characterized by the development of vesico-bullous lesions.
ORPHA:33408
Classification level: Disorder- Synonym(s): -
- Prevalence: Unknown
- Inheritance: Autosomal dominant or Not applicable
- Age of onset: Childhood
- ICD-10: L43.1
- OMIM: -
- UMLS: C0023648
- MeSH: -
- GARD: -
- MedDRA: 10056960
Summary
Epidemiology
Prevalence is unknown and only a few cases, both sporadic and familial, have been described in the literature.
Clinical description
The disease manifests during childhood or adolescence. Bullous lesions develop on top of preexisting lichen planus papules or on normal skin and generally affect the lower limbs or the lower mucosal lip, and in some rare cases the torso. In this condition, the epithelium separates from the dermis. In the case of oral bullous lichen planus, the vesicles and bullae burst soon after they appear which results in erosions.
Etiology
Etiology is unknown.
Additional information
Further information on this disease
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