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Disease definition

Cholangiocarcinoma (CCA) is a biliary tract cancer (BTC, see this term) originating in the epithelium of the biliary tree, either intra or extra hepatic.


Classification level: Disorder
  • Synonym(s):
    • Bile duct cancer
    • CCA
  • Prevalence: 1-9 / 100 000
  • Inheritance: Not applicable 
  • Age of onset: Adult
  • ICD-10: C22.1  C24.0  C24.8  C24.9
  • OMIM: 615619
  • UMLS: C0206698  C0740277
  • MeSH: D001650  D018281
  • GARD: 9304
  • MedDRA: 10004593  10008593

Detailed information

Article for general public


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