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Bazex-Dupré-Christol syndrome

Disease definition

Bazex-Dupré-Christol syndrome is a rare genodermatosis with a predisposition to early-onset basal cell carcinomas.


Classification level: Disorder
  • Synonym(s):
    • BDCS
    • Follicular atrophoderma and basal cell carcinomas
  • Prevalence: <1 / 1 000 000
  • Inheritance: X-linked dominant 
  • Age of onset: Infancy, Neonatal
  • ICD-10: L98.8
  • OMIM: 301845
  • UMLS: C0346104
  • MeSH: C537663
  • GARD: 838
  • MedDRA: -
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