Orphanet: Brugada syndrome

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Brugada syndrome

Disease definition

A cardiac disorder characterized on electrocardiogram (ECG) by ST segment elevation with a coved aspect on the right precordial leads, and a clinical susceptibility to ventricular tachyarrhythmias and sudden death occurring in the absence of overt myocardial abnormalities.


Classification level: Disorder
  • Synonym(s):
    • Idiopathic ventricular fibrillation, Brugada type
  • Prevalence: 1-5 / 10 000
  • Inheritance: Autosomal dominant or Not applicable 
  • Age of onset: Adult, Childhood
  • ICD-10: I49.8
  • OMIM: 601144  611777  611875  611876  612838  613119  613120  613123  616399
  • UMLS: C1142166  C1955837
  • MeSH: D053840
  • GARD: 1030
  • MedDRA: 10059027

Detailed information


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