Orphanet: Bronchiolitis obliterans with obstructive pulmonary disease
x

Search for a rare disease

* (*) mandatory field

Other search option(s)

Suggest an update

(*) Required fields.

Attention

Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. For all other comments, please send your remarks via contact us. Only comments written in English can be processed.

Captcha image

Bronchiolitis obliterans with obstructive pulmonary disease

Disease definition

Bronchiolitis obliterans syndrome (BOS) is a lung disorder that is mainly associated with chronic allograft dysfunction after lung transplantation and that is characterized by inflammation and fibrosis of bronchiolar walls that reduce the diameter of the bronchioles and result in progressive and irreversible airflow obstruction.

ORPHA:1303

Classification level: Disorder
  • Synonym(s):
    • Constrictive bronchiolitis
    • Obliterative bronchiolitis
  • Prevalence: Unknown
  • Inheritance: Not applicable 
  • Age of onset: All ages
  • ICD-10: J44.8
  • OMIM: -
  • UMLS: C0006272  C2350875
  • MeSH: -
  • GARD: 5961
  • MedDRA: -
The documents contained in this web site are presented for information purposes only. The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment.